Table 2. SJIA diagnostic criteria: PRINTO and ILAR [11,12]

PRINTO	ILAR
Fever ≥ 2 weeks	Fever ≥ 2 weeks
(Major criteria)
1. Arthritis	Arthritis
	≥ 1/4 following criteria
2. Evanescent erythematous rash	1. Evanescent erythematous rash
(Minor criteria)
1. Generalized lymphadenopathy	2. Generalized lymphadenopathy
or HM ± SM	3. HM ± SM
2. Serositis1)	4. Serositis1)
3. Arthralgia ≥ 2 weeks
4. Leukocytosis ≥ 15,000 /mm3
Fever + (2 major or [1 major + 2 minor])	Fever + Arthritis + ≥ 1/4 criteria

Serositis: pericarditis, pleuritis, or peritonitis.
SJIA: systemic juvenile idiopathic arthritis; PRINTO: Paediatric Rheumatology International Trials Organisation; ILAR: International League of Associations for Rheumatology; HM: hepatomegaly; SM: splenomegaly.