Age (months) | 58.08 | 66.56 | 38.83 | 53.55 | 25.56 |
Clinical presentation | Complete | Complete | Complete | Complete | Complete |
Recurrent illness | Yes (5mo) | No | No | No | No |
Tx (fever day) | 1st | IVIG (D5) | IVIG (D6) | IVIG (D5) | IVIG (D6) | IVIG (D4) |
2nd | IVIG (D8) | IVIG+mPD (D7) | IVIG+mPD (D8) | IVIG+mPD (D10) | IVIG (D6) |
3rd | mPD (D9) | PE (D14) | PE (D14) | Infliximab (D14) | mPD (D9) |
4th | Infliximab (D14) | | | PE (D15) | PE (D13) |
5th | PE (D16) | | | | |
CAA (mm (z score)) | Pre-IVIG | Normal | Normal | Normal | Normal | Normal |
Post-IVIG | Normal | | | | Normal |
Pre-PE | AN (D14)LAD (3.06(2.63)) | AN (D14)RCA (4.13(3.31)) | Normal | AN (D14)LAD (6.2(6.56))LMCA (4.47(3.90)RCA (4.1(3.58)) | Normal |
Follow up <3 month | ANLAD (6.25(6.56))GARCA (9(7.47)) | Resolved | Normal | ANLMCA (3.6(2.55))RCA (3.1(2.68))GA | Normal |
Follow up 1 year | ANLAD (4.6(4.62))GARCA (9.3(7.42)) | Normal | Normal | LAD (8.2(6.98)) ResolvedLMCA, RCAGALAD (8.7(8.16)) | Normal |