Table 1. Clinical characteristics of five subjects treated with plasma exchange

Subject number No. 1 No. 2 No. 3 No. 4 No. 5
Age (months) 58.08 66.56 38.83 53.55 25.56
Clinical presentation Complete Complete Complete Complete Complete
Recurrent illness Yes (5mo) No No No No
Tx (fever day) 1st IVIG (D5) IVIG (D6) IVIG (D5) IVIG (D6) IVIG (D4)
2nd IVIG (D8) IVIG+mPD (D7) IVIG+mPD (D8) IVIG+mPD (D10) IVIG (D6)
3rd mPD (D9) PE (D14) PE (D14) Infliximab (D14) mPD (D9)
4th Infliximab (D14) PE (D15) PE (D13)
5th PE (D16)
CAA (mm (z score)) Pre-IVIG Normal Normal Normal Normal Normal
Post-IVIG Normal Normal
Pre-PE AN (D14)LAD (3.06(2.63)) AN (D14)RCA (4.13(3.31)) Normal AN (D14)LAD (6.2(6.56))LMCA (4.47(3.90)RCA (4.1(3.58)) Normal
Follow up <3 month ANLAD (6.25(6.56))GARCA (9(7.47)) Resolved Normal ANLMCA (3.6(2.55))RCA (3.1(2.68))GA Normal
Follow up 1 year ANLAD (4.6(4.62))GARCA (9.3(7.42)) Normal Normal LAD (8.2(6.98)) ResolvedLMCA, RCAGALAD (8.7(8.16)) Normal
Tx: treatment; IVIG: intravenous immunoglobulin; mPD: methyl prednisolone; PE: plasma exchange; CAA: coronary artery abnormality; LMCA: left main coronary artery; LAD: left anterior descending coronary artery; RCA: right coronary artery; AN: aneurysm; GA: giant aneurysm.