Table 2. Diagnostic guidelines for Kawasaki disease in Japan

Principal clinical features1. Fever.2. Bilateral bulbar conjunctival injection.3. Changes of lips and oral cavity: reddening of lips, strawberry tongue, diffuse injection of oral and pharyngeal mucosa.4. Rash (including redness at the site of Bacille Calmette-Guèrin [BCG] inoculation).5. Changes of peripheral extremities: (Initial stage) reddening of palms and soles, edema. (Convalescent stage) periungual desquamation.6. Non-suppurative cervical lymphadenopathy.
Complete Kawasaki disease• A patient who fulfills the criteria with five or six signs.• A patient who fulfills the criteria with four signs and coronary artery abnormality by echocardiography;- Z-score ≥ 2.5; or inner diameter ≥ 3 mm (< 5 years old) or ≥ 4 mm (≥ 5 years old)
Incomplete Kawasaki disease• A patient who has three principal clinical features with coronary artery abnormality by echocardiography and in whom other febrile illnesses have been excluded.• A patient who has three or four principal clinical features without coronary artery dilation and any evidence of other febrile illnesses but with some features of other significant clinical features.• Incomplete KD may also be considered in the presence of only one or two principal clinical features after excluding other diagnoses.
KD: Kawasaki disease.